Correção de deformidade em varo da tíbia em osteocondromatose múltipla hereditária com fixador externo hexapodal tipo SUV
Keywords:
exostosis, hereditary multiple osteochondromatosis, osteochondromaAbstract
Hereditary Multiple Osteochondromatosis (HMO) or Multiple Exostosis, is a rare autosomal dominant disease 1 in 50.000 individuals. There are multiples benigns tumors from cartilaginous origin. We describe a patient diagnosed with HMO with deformities that required surgical intervention. This study presents treatment of varus deformity on the right leg corrected by proximal tibia osteotomy and use of hexapodal external fixator Ortho SUV Frame® with gradual correction.
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References
El-Husny AS, et al. Osteocondromatose Múltipla Hereditária: relato de um caso clínico familiar. Revista Científica Multidisciplinar Núcleo do Conhecimento. Ano 04, Ed. 12, Vol.07, pp. 24-29. dez.; 2019.
Souza AMG, Bispo Júnior RZ. Osteocondroma: Ignorar ou Investigar? Rev Bras Ortop.49(6):555-64; 2014.
David A, Dalmina V, Souza V, Jr. CP, Oliveira GK. Exostose múltipla hereditária. Rev Bras Ortop. 30(11/12); 1995.
Guerrero TP, Fonseca JEG, Duany LFA. Osteocondromatosis múltiple. Caso clínico. Multimed, Granma, v. 24, n. 3, p. 680-689, jun.; 2020.
Alabdullrahman LW, Byerly DW. Osteochondroma. StatPearls [Internet] Treasure Island (FL). 2021 Jan [cited 2021 Aug 15]. Available from: https://www.ncbi.nlm.nih.gov/books/NBK544296/
Ruiz Jr. RL et al. Osteocondomatose múltipla hereditária com envolvimento costal. Rev. Col. Bras. Cir., Rio de Janeiro, v. 35, n. 4, p. 277-279, aug; 2008.
Arms DM, Strecker WB, Manske PR, Schoenecker PL. Management of Forearm Deformity in Multiple Hereditary Osteochondromatosis. [Miscellaneous Article] Journal of Pediatric Orthopaedics. 17(4):450-454, July/August; 1997.
Rodrigues FL, Aita MA, R ebolledo DCS, Bernardo RM. Alongamento da ulna associado à reconstrução ligamentar damembrana interóssea na exostose cartilaginosa múltipla. Rev Técnicas em Ortopedia. 2016;16(4):2-7.
Pacifici M. Hereditary Multiple Exostoses: New Insights into athogenesis, Clinical Complications, and Potential Treatments. Current osteoporosis reports, 15(3), 142-152; 2017.
Hameetman L, Bovée JV, Taminiau AH, Kroon HM, Hogendoorn PC. Multiple osteochondromas: clinicopathological and genetic spectrum and suggestions for clinical management. Hereditary cancer in clinical practice, 2(4), 161-173; 2004.
Bovée JV. Multiple osteochondromas. Orphanet J Rare Dis 3, 3; 2008.
Beutel BG, Klifto CS, Chu A. Timing of forearm deformity correction in a child with multiple hereditary exostosis. American journal of orthopedics (Belle Mead, N.J.), 43(9), 422-425.3; 2014.
Grzelecki D, Szneider J, Marczak D, et al. Total knee arthroplasty with simultaneous tibial shaft osteotomy in patient with multiple hereditary osteochondromas and multiaxial limb deformity – a case report. BMC Musculoskelet Disord 21, 233; 2020.
Lee, J., Rathod, C., Park, H., Lee, H., Rhee, I., & Kim, H. Longitudinal Observation of Changes in the Ankle Alignment and Tibiofibular Relationships in Hereditary Multiple Exostoses. Diagnostics (Basel), 10(10), 752; 2020.
Oosterbos M, Zwan AL, Woude HJ, Ham S J. Correction of ankle valgus by hemiepiphysiodesis using the tension band principle in patients with multiple hereditary exostosis. Journal of children’s orthopaedics, 10(3), 267-273; 2016.
