Tratamento de deformidade em varo dos membros inferiores em acondroplasia
Keywords:
Achondroplasia, Genu varum, Short limbs, Hemiepiphyisiodesis, External FixatorsAbstract
The patient reported had achondroplasia, bone dysplasia responsible for the most common form of rhizomelic dwarfism. Among the most common clinical features, shorter limbs with consequent short stature, ligament laxity and angular deformities of the lower limbs, especially genu varum. The aim of this article is to describe the orthopedic treatment for genu varum, including tibial osteotomies and stabilization with circular external fixator for gradual correction of the deformity and bone lengthening, followed by lateral hemiepiphysiodesis of the distal femur and proximal tibia of both limbs and at last, valgus osteotomy of the right distal femur with acute correction and stabilization with monolateral external fixator.
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