Vertebrectomia total posterior estadiada para correção de escoliose congenita
Keywords:
scoliosis, congenital, surgery, osteotomyAbstract
Congenital kyphoscoliosis is a very complex pathology, due to its rapid progression, degree of severity, and also due to the association with other congenital syndromes, which makes its treatment quite challenging. We present a case of a 19-year-old patient with severe congenital kyphoscoliosis, who had already undergone an unsuccessful attempt with a surgical treatment in childhood. We describe the use of the posterior total osteotomy of VCR (Vertebral Column Ressection) type for the treatment of the case. We discussed the use of the technique, its potential complications and the evolution of the case during and after treatment.
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References
Quan L, Smith DW. The VATER association. Vertebral defects, anal atresia, T-E fistula with esophageal atresia, radial and renal dysplasia: a spectrum of associated defects. J Pediatr.
;82(1):104-107.
Nora AH, Nora JJ. A syndrome of multiple congenital anomalies associated with teratogenic exposure. Arch Environ Health. 1975; 30(1):17-21.
Dunham AM, Sponseller PD. Congenital Scoliosis. In: Garfin S, Eismont F, Bell G, Bono C, Fischgrund J (eds). Rothman-Simeone and Herkowitz’s The Spine. 7th ed. Philadelphia: Elsevier; 2018. p. 435-50.
Kaspiris A, Grivas TB, Weiss HR, Turnbull D. Surgical and conservative treatment of patients with congenital scoliosis: a search for long-term results. Scoliosis. 2011;6-12.
Schwab F, Blondel B, Chay E, Demakakos J, Lenke L, Tropiano P, et al. The comprehensive anatomical spinal osteotomy classification. Neurosurgery. 2014;74(1):112-20;
Hedequist D, Emans J. Congenital scoliosis. a review and update. J Pediatr Orthop. 2007;27(1):106-116.
Marks DS, Qaimkhani SA. The natural history of congenital scoliosis and kyphosis. Spine. 2009;34(17):1751-5.
Suk SI, Kim JH, Kim WJ, et al. Posterior vertebral column resection for severe spinal deformities. Spine. 2002;27(21):2374-82.
Lenke LG, Sides BA, Koester LA, Hensley M, Blanke KM. Vertebral column resection for the treatment of severe spinal deformity. Clin Orthop Relat Res. 2010;468(3):687-99.
Saifi C, Laratta JL, Peridis P, Shillingford JN, Lehamn RA, Lenje LG. Vertebral Column Resection for Rigid Spinal Deformity. Global Spine Journal. 2017;7(3):280-90.